History
This 3 year old boy has a history of extreme chin-up head posturing and droopy eyelids since infancy.
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Marked chin-up head posture Bilateral ptosis Bilateral brow elevation Bilateral primary position hypotropia |
Congenital bilateral inferior rectus fibrosis syndrome
Surgery #1:
Bilateral inferior rectus recession 6 mm (muscles had tight fibrotic consistency and forced duction test was markedly positive OU.
Bilateral frontalis sling using autogenous fascia lata.
Surgery #2:
Bilateral lateral rectus recession 7 mm.
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